Atypical Neurofibromatous Neoplasms of Uncertain Biological Potential in Children with Neurofibromatosis Type 1: Report of Two Patients and Review

Nelly Marlene Román-Mendoza, Eunate Martí-Carrera, Daniel Azorín-Cuadrillero, Luis Blasco-Santana, Marta Escribano-Pérez, Felisa Vázquez-Gómez, Fernando Martín-del-Valle, Anna Duat-Rodríguez, Ángela Hernández-Martín

International Journal of Surgical Pathology

Published online on May 15, 2026

Abstract

International Journal of Surgical Pathology, Ahead of Print.
Atypical neurofibromatous neoplasm of uncertain biological potential (ANNUBP) lies between plexiform neurofibroma and malignant peripheral nerve sheath tumor (MPNST) in neurofibromatosis type 1 (NF1). Pediatric data are limited. We report two children ...